4-Methylumbelliferyl-alpha-L-iduronic acid, cyclohexylammonium salt

Catalog
Description
Size
Price(USD)
Qty
Catalog
RC-377
RC-377
Description
4-Methylumbelliferyl-alpha-L-iduronic acid, cyclohexylammonium salt
4-Methylumbelliferyl-alpha-L-iduronic acid, cyclohexylammonium salt
Size
25 mg
25 mg
$2,351.00
$2,351.00
4-Methylumbelliferyl-α- L-iduronic acid cyclohexylammonium salt
4-Methylumbelliferyl-α-L-iduronide.
4-MU-α-L-IdoA • CHX
MOLECULAR BIOLOGY GRADE
Off-white powder
Fluorogenic soluble enzyme substrate for α-L-iduronidase. α-L-iduronidase is deficient in the genetic disorder Mucopolysaccharidosis type I, also called Hurler syndrome. Diagnosis of Hurler syndrome involves enzymatic assay of α-L-iduronidase activity using the fluorogenic enzyme substrate 4-Methylumbelliferyl-α-L-iduronide.
Store at -15°C in a dark, dry place.
Features
- CAS#: 66895-33-8
- Molecular Formula: C16H16O9·C6H13N
- Molecular Weight: 451.48 g/mol