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ITT0977

ITT0977
  • Catalog: ITT0977
  • Gene/Protein: CLN6
  • Product Description: Immunotag™ CLN6 Polyclonal Antibody
385.0000
Price in reward points: 385

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Immunotag™ CLN6 Polyclonal Antibody
Antibody Specification
Datasheet
Target Protein CLN6
Clonality Polyclonal
Storage/Stability -20°C/1 year
Application WB,IHC-p,ELISA
Recommended Dilution Western Blot: 1/500 - 1/2000. Immunohistochemistry: 1/100 - 1/300. ELISA: 1/40000. Not yet tested in other applications.
Concentration 1 mg/ml
Reactive Species Human
Host Species Rabbit
Immunogen The antiserum was produced against synthesized peptide derived from human CLN6. AA range:221-270
Specificity CLN6 Polyclonal Antibody detects endogenous levels of CLN6 protein.
Purification The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen
Form Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
Gene Name CLN6
Accession No. Q9NWW5
Alternate Names CLN6; Ceroid-lipofuscinosis neuronal protein 6; Protein CLN6
Description ceroid-lipofuscinosis, neuronal 6, late infantile, variant(CLN6) Homo sapiens This gene is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function. [provided by RefSeq, Oct 2008],
Protein Expression Epithelium,Lung,Urinary bladder,
Subcellular Localization endoplasmic reticulum,endoplasmic reticulum lumen,endoplasmic reticulum membrane,membrane,integral component of membrane,
Protein Function disease:Defects in CLN6 are the cause of variant late-onset infantile neuronal ceroid lipofuscinosis (vLINCL) [MIM:601780].,online information:Neural Ceroid Lipofuscinoses mutation db,
Usage For Research Use Only! Not for diagnostic or therapeutic procedures.
Material Safety Data Sheet
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